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Primary Pulmonary Hypertension
Pulmonary hypertension (PH) is a disease characterized by elevated by pulmonary artery pressure, which often results in right ventricular failure. It is defined by a mean pulmonary artery pressure (PAP) = 25 mmHg at rest as assessed by right heart catheterization (RHC). Primary hypertension (PPH) is a clinical syndrome of pulmonary hypertension that progresses rapidly to right ventricular failure and death. The frequency of diagnosis of PPH among patients undergoing right heart cathterization (RHC) has been reported to be about 1%. The incidence is between the ages of 20 and 45 years. The ratio of women to men was 1.7: 1 regardies to age at diagnosis. Clinical manifestation is dysoeneu (60%), fatique, chest pain, syncope, and leg edema. The physical findings are typical of any patient with pulmonary hypertension. An increase in the pulmonic component o the second heart sound and a right – sided fourth heart sound are early findings. Tricuspid regurgitation is also very common. Peripheral cyanosis and edema are often. Diagnosticevaluations are ECG, CXR, Echecardiography, Thoras CT Scanning, and RHC. There is no cure for PPH, nor is there a therapeutic approach which is uniformly accepted or succesful. It is about a-30 year old-man. Acehnese with chief complaint was dyspnoe, fatique, syncope, chest pain, distended abdomen and swelling legs. The clinical presentation was tachycardia, distention of jugular vein, pansystolic murmur with gradion 4/6 on the tricuspid area, p2>A2, ascites with hepatomegali and edema of inferior extrenities. The diagnosis was established by anamnesis, clinical presentation, ECG, CXR,Echocardiography and Thorax CT scanning as PPH WHO-FC IV. After treatment, he had been improved clinically and became out patient after 10 days.
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