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Iktiosis Lamelaria
Lamellar ichthyosis is a rare autosomal recessive disorder, It is characterized by a colodion membrane that may wrap the infant at birth. The membrane dries out and graduallly sheds in a large sheet-like layer. Furthermore, a redness residual left with hyperkeratosis. This paper reports the management of a rare case of lamellar ichthyosis. A one-day-old baby, was born as an infant with dry, rigid, hard skin, parckmen-like appearance. The skin was graduallly shed with large yellowish squama in erithematous base almost on the whole body, face, extremities, palms and soles. Furthermore, another signs are ectropion eyes, eclabium mouth and shrinked ears. The management of lamellar ichthyosis involved good intensive neonatal care, fluid electrolyte balance, antibiotic and topical emollient. Six months after the therapy, the skin turned to normal. Furthermore, the growth and the development were appropriate to their age. Finally, it could be concluded that a good intensive care showed an excellent result.
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