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Sindrom Prune Belly pada Anak (Prune Belly Syndrome)

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Prune belly syndrome (PBS) is a congenital anomaly syndrome characterized by triad of abdominal musculature deficiency and malous development of the urinary tract and bilateral cryptorchidsm. The syndrome seems to be sporadic affecting predominantly boys Etiopathophysio logy of PBS remains unknown but may be caused by primary mesodermal development defect. PBS can be defect. PBS can be detected intrauterine with fetal ultrasound and in newborn with typical triad of clinical features consist of winkled appearance of the abdominal skin mimicking a prune fruit, bilateral cryptorchidism, and blader distension. Radioogic finding could detect present defects. Management includes supportive therapy and surgical intervention. Prognosis depends on the degree of pulmonary and renal dysplasia, degree of urinary tract obstruction,and severity tract infection.

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Series Title

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Call Number

Cermin Dunia Kedokteran,36((7):498-501

Publisher

Jakarta : Kalbe Farma., 2009

Collation

4p.

Language

ISBN/ISSN

0125-913X

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Content Type

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Media Type

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Carrier Type

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Edition

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Subject(s)

PRUNE BELLY SYNDROME

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